Pulmoner Arter Sarkomunun Multi-modalite Görüntüleme ile Değerlendirilmesi

¹Department of Cardiology, Kartal Koşuyolu Training and Research Hospital, İstanbul, Turkey
²Department of Pathology, Marmara University School of Medicine, İstanbul, Turkey
³Department of Thoracic Surgery, Kartal Koşuyolu Training and Research Hospital, İstanbul, Turkey
⁴Department of Cardiovascular Surgery, Koşuyolu Training and Research Hospital, İstanbul, Turkey

Pulmoner arter sarkomu, kötü prognozlu seyreden, son derece nadir görülen bir malignitedir. Spesifik olmayan belirti ve bulguların yanı sıra benzer görüntüleme bulguları nedeni ile pulmoner tromboembolik hastalıktan ayrımı zordur. Bu olguda, başta astım tanısı alan, daha sonra PAS tanısı koyulan, 46 yaşında bir erkek hastayı sunmaktayız. Hastada pulmoner arterde kitle, yayılımı, mobilitesi ve invazyonu, arter duvarına tutunması, multi-modalite görüntüleme ile değerlendirildi. Pulmoner arter kitlesi eksize edilerek pulmoner endarterektomi yapıldı. Histopatolojik olarak pleomorfik morfolojiye sahip farklılaşmamış sarkom tanısı koyuldu.

Anahtar Kelimeler:

Diagnosis of Pulmonary Artery Sarcoma with Multi-modality Imaging

Pulmonary artery sarcoma is an extremely uncommon malignancy with a poor prognosis. It is often difficult to distinguish it from pulmonary thromboembolic disease because of nonspecific signs and symptoms as well as similar imaging findings. We present a 46-year-old man
who had initially been diagnosed with presumed asthma that later proved to be pulmonary artery sarcoma. The patient was evaluated with multi-modality imaging studies which showed a mass in the pulmonary artery, its extension, mobility and invasion, and attachment to the
artery wall. Pulmonary artery mass was excised and pulmonary artery endarterectomy was performed. The histopathological diagnosis was undifferentiated sarcoma with pleomorphic morphology.

Keywords:

Büşra Güvendi Şengör, Alev Kılıçgedik, Tuba Unkun, Emine Bozkurtlar, Ahmet Erdal Taşçı, Serpil Taş, Cevat Kırma. Diagnosis of Pulmonary Artery Sarcoma with Multi-modality Imaging. . 2022; 50(2): 155-158

Sorumlu Yazar: Büşra Güvendi Şengör, Türkiye