. 2024; 41(2): 97-104 | DOI: 10.4274/tjh.galenos.2024.2024.0055 | |||
Management of Adult Primary Immune Thrombocytopenia: Delphi- Based Consensus RecommendationsAhmet Muzaffer Demir1, Elif Gülsüm Ümit1, Muhlis Cem Ar2, Mesut Ayer3, Meltem Aylı4, Volkan Karakuş5, Emin Kaya6, Fahir Özkalemkaş7, Nilgün Sayınalp8, Mehmet Sönmez9, Fahri Şahin10, Selami Koçak Toprak11, Tayfur Toptaş12, İrfan Yavaşoğlu13, Ümran Çalış141Trakya University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Edirne, Türkiye2İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İstanbul, Türkiye 3University of Health Sciences Türkiye, Başakşehir Çam and Sakura City Hospital, Clinic of Hematology, İstanbul, Türkiye 4University of Health Sciences, Gülhane Training and Research Hospital, Clinic of Internal Medicine, Division of Hematology, Ankara, Türkiye 5University of Health Sciences Türkiye, Antalya Training and Research Hospital, Clinic of Hematology, Antalya, Türkiye 6İnönü University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Malatya, Türkiye 7Bursa Uludağ University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Bursa, Türkiye 8Hacettepe University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Ankara, Türkiye 9Karadeniz Technical University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Trabzon, Türkiye 10Ege University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İzmir, Türkiye 11Ankara University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Ankara, Türkiye 12Marmara University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İstanbul, Türkiye 13Aydın Adnan Menderes University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Aydın, Türkiye 14Abdi İbrahim İlaç Sanayi ve Tic. A.Ş., Senior Medical Manager, İstanbul, Türkiye Objective: Primary immune thrombocytopenia (pITP) is an acquired autoimmune disorder related to the increased destruction and/or impaired production of platelets. Its diagnosis and management are challenging and require expertise and the interpretation of international consensus reports and guidelines with national variations in availability. We aimed to assess the agreement of hematologists in Türkiye on certain aspects of both first-line and second-line management of patients with pITP. Erişkin Primer İmmün Trombositopeni Yönetimi: Delphi-Temelli Uzlaşı ÖnerileriAhmet Muzaffer Demir1, Elif Gülsüm Ümit1, Muhlis Cem Ar2, Mesut Ayer3, Meltem Aylı4, Volkan Karakuş5, Emin Kaya6, Fahir Özkalemkaş7, Nilgün Sayınalp8, Mehmet Sönmez9, Fahri Şahin10, Selami Koçak Toprak11, Tayfur Toptaş12, İrfan Yavaşoğlu13, Ümran Çalış141Trakya University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Edirne, Türkiye2İstanbul University-Cerrahpaşa, Cerrahpaşa Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İstanbul, Türkiye 3University of Health Sciences Türkiye, Başakşehir Çam and Sakura City Hospital, Clinic of Hematology, İstanbul, Türkiye 4University of Health Sciences, Gülhane Training and Research Hospital, Clinic of Internal Medicine, Division of Hematology, Ankara, Türkiye 5University of Health Sciences Türkiye, Antalya Training and Research Hospital, Clinic of Hematology, Antalya, Türkiye 6İnönü University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Malatya, Türkiye 7Bursa Uludağ University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Bursa, Türkiye 8Hacettepe University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Ankara, Türkiye 9Karadeniz Technical University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Trabzon, Türkiye 10Ege University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İzmir, Türkiye 11Ankara University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Ankara, Türkiye 12Marmara University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, İstanbul, Türkiye 13Aydın Adnan Menderes University Faculty of Medicine, Department of Internal Medicine, Division of Hematology, Aydın, Türkiye 14Abdi İbrahim İlaç Sanayi ve Tic. A.Ş., Senior Medical Manager, İstanbul, Türkiye Amaç: Primer immün trombositopeni (pITP), trombositlerin artan yıkımı ve/veya bozulmuş üretimi ile ilişkili edinsel bir oto-immün hastalıktır. pITP’nin tanı ve yönetimi zorludur; ayrıca hem uzmanlık hem de uluslararası fikir birliği raporları ile kılavuzlarının, ulusal farklılıkları da göz önünde bulundurarak, yorumlanmasını gerektirir. Bu çalışmada Türkiye’deki hematologların pITP hastalarının birinci ve ikinci basamak tedavisinin belirli alanlarındaki fikir birliği düzeylerini değerlendirmeyi amaçladık. Ahmet Muzaffer Demir, Elif Gülsüm Ümit, Muhlis Cem Ar, Mesut Ayer, Meltem Aylı, Volkan Karakuş, Emin Kaya, Fahir Özkalemkaş, Nilgün Sayınalp, Mehmet Sönmez, Fahri Şahin, Selami Koçak Toprak, Tayfur Toptaş, İrfan Yavaşoğlu, Ümran Çalış. Management of Adult Primary Immune Thrombocytopenia: Delphi- Based Consensus Recommendations. . 2024; 41(2): 97-104 Corresponding Author: Ahmet Muzaffer Demir |
|