. 2009; 24(2): 92-94 | |||
Caroli’s disease: A case reportAli Karaman1, Doğan Nasır Binici2, İhsan Doru31Erzurum Nenehatun Maternity Hospital, Genetics Unit, Erzurum2Erzurum Nenehatun Maternity Hospital, Internal Medicine Clinic, Erzurum 3Erzurum Regional Training and Research Hospital, Radiology Unit, Erzurum Caroli’s disease is a rare congenital disorder characterized by cytic dilatation of the intrahepatic bile ducts. Caroli’s disease is transmitted in autosomal recessive fashion. Chollangitis, liver cirrhosis, and cholangiocarcinoma are its potantial complications. The magnetic resonance cholangiography (MRCG) is the metod with the highest sensitivity in the diagnosis of Caroli’s disease. In this study, we present a case of a fifty year old grill who was diagnosid with Caroli’s disease (Caroli type I). Keywords: Liver, biliary tract, cystic disease, caroli’s diseaseCaroli hastalığı: Bir olgu sunumuAli Karaman1, Doğan Nasır Binici2, İhsan Doru31Erzurum Nenehatun Kadın Doğum Hastanesi, Genetik Ünitesi, Erzurum2Erzurum Nenehatun Kadın Doğum Hastanesi, İç hastalıkları Kliniği, Erzurum 3Erzurum Bölge Eğitim ve Araştırma Hastanesi, Radyoloji Ünitesi, Erzurum Anahtar Kelimeler: Karaciğer, safra yolları, kistik hastalık, caroli hastalığı Ali Karaman, Doğan Nasır Binici, İhsan Doru. Caroli’s disease: A case report. . 2009; 24(2): 92-94 Corresponding Author: Ali Karaman, Türkiye |
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