%PDF-1.3
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q
0 0.89 595 841 re
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1 g
0 841.89 0 0 re
f
Q
/GS1 gs
q
0 0 0 0 k
56.693 150.237 481.89 442.204 re
f
Q
q
BT
/F0 1 Tf
9 0 0 9 148.0765 584.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(SUMMARY)Tj
ET
Q
q
BT
/F1 1 Tf
9 0 0 9 146.4593 564.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Fahr disease)Tj
ET
Q
q
BT
/F2 1 Tf
9 0 0 9 57.6929 544.4233 Tm
0 Tr
0 0 0 1 k
0 Tc
0.048 Tw
(Fahr disease is a disorder that is characterised with the mas-)Tj
0 -1.11112 TD
0.001 Tc
0.124 Tw
(sive calcification in cerebral basal ganglions or cerebellum.)Tj
0 -1.11111 TD
0.02 Tc
0.105 Tw
(Clinical findings vary from minimal motional disorders to)Tj
T*
0 Tc
0.115 Tw
(convulsions and may be sporadic, familial or idiopatic. Also)Tj
T*
0.018 Tw
(this disease may be related with hypoparathyroidism or defect)Tj
0 -1.11112 TD
0 Tw
(of free radical production or iron transportion.)Tj
0 -2.22222 TD
0.099 Tw
(13 year old boy patient who has unvoluntary contractions in)Tj
0 -1.11111 TD
0.124 Tw
(his hands, feet and face during the last month attended to a)Tj
T*
0.006 Tc
0.119 Tw
(private hospital. Bilateral symetric widespread calcification)Tj
T*
0 Tc
0.014 Tw
(in subcortical area and basal ganglions has been seen in CCT)Tj
-0.0001 Tc
(and)'
1.75809 0 Td
0 Tc
0.008 Tw
(the patient has been sent to our unit. In physical examina)Tj
22.99489 0 TD
(-)Tj
-24.75299 -1.11112 TD
0.077 Tw
(tion; his coreatetoic motions has been seen. Laboratory find-)Tj
0 -1.11111 TD
0.039 Tw
(ings; Ca: 7.2 mg/dl, P: 6.8 mg/dl, ALP: 499 U/l, Serum PTH:)Tj
T*
0 Tw
(381 pg/ml (N: 12-72 pg/ml).)Tj
0 -2.22223 TD
0.032 Tw
(In his cranial MRI investigation: T1 hyperintention in bilater-)Tj
0 -1.11111 TD
0.112 Tw
(al dental nucleus, putamen and caudat nucleus and symetric)Tj
T*
0.001 Tc
0.124 Tw
(signal increase especially in basal ganglions has been seen.)Tj
T*
0 Tc
0.041 Tw
(The patient has been accepted as pseudohypoparathyroid and)Tj
T*
0.002 Tc
0.122 Tw
(treated with calsitriol and calsium lactate. This case is pre-)Tj
T*
0 Tc
0.067 Tw
(sented in order to discuss the relationship between intracere-)Tj
T*
0 Tw
(bral calsifications and endocrinopathies. )Tj
ET
Q
q
BT
/F0 1 Tf
9 0 0 9 57.6929 304.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Key words: )Tj
ET
Q
q
BT
/F2 1 Tf
9 0 0 9 101.1834 304.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Fahr disease, pseudohypoparathyroidism)Tj
ET
Q
q
BT
/F0 1 Tf
9 0 0 9 57.6929 284.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Anahtar kelimeler:)Tj
ET
Q
q
BT
/F2 1 Tf
9 0 0 9 130.6839 284.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Fahr hastal\335\333\335, pseudohipoparatiroidi)Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 57.6929 245.4232 Tm
0 Tr
0 0 0 1 k
0 Tc
0.093 Tw
(Fahr sendromu, serebral korteks ve bazal gangliyonlar\335)Tj
0 -1.3 TD
0 Tw
(da i\215eren beynin baz\335 b\232lgelerinde anormal kalsiyum bi)Tj
22.2444 0 TD
(-)Tj
-22.2444 -1.30001 TD
0.094 Tw
[(rikimi ile karakterize ailesel)-344(bir hastal\335kt\335r )]TJ
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 233.7784 222.0632 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((1))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 243.1026 219.4232 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(.)Tj
0.5933 0 Td
0 Tc
0 Tw
(Bilateral)Tj
-19.13427 -1.3 TD
0.125 Tw
(simetrik intraserebral kalsifikasyon, serebral idiyopatik)Tj
T*
0 Tw
(aterosklerotik )Tj
5.85871 0.00001 TD
(olmayan )Tj
3.80475 0.00001 TD
(kalsifikasyon, )Tj
5.94318 0.00001 TD
(ailesel)Tj
2.91535 0 TD
(id)Tj
0.77783 0 TD
(i)Tj
0.27784 0.00001 TD
(yopatik)Tj
-19.57766 -1.30004 TD
0.005 Tc
0.12 Tw
(ferrokalsinosis, ekstrapiramidal demir-kalsiyum biriki-)Tj
0 -1.3 TD
0.006 Tc
0.119 Tw
[(mi sendromu gibi adlar da)-375(verilmektedir. Triad; bazal)]TJ
T*
0.002 Tc
0.123 Tw
(gangliyonlarin simetrik kalsifikasyonlar\335, n\232ropsikiyat-)Tj
25.41181 42.91885 TD
0.004 Tc
0.121 Tw
(rik semptomlar ve paratiroid bezin disfonksiyonu \337ek-)Tj
0 -1.3 TD
0.008 Tc
0.117 Tw
(lindedir. Motor fonksiyon bozuklu\333u, demans, mental)Tj
T*
0.003 Tc
0.122 Tw
(retardasyon, spastik paralizi, dizartri, spastisite, g\232rme)Tj
0 -1.30001 TD
0.001 Tc
0.124 Tw
(bozuklu\333u, istemsiz yaz\335 yazma tarz\335nda atetotik hare-)Tj
0 -1.3 TD
0.007 Tc
0.118 Tw
(ketler, parkinsonizmde g\232r\237len tremor, rijidite, maske)Tj
T*
0.009 Tc
0.115 Tw
(y\237z\237, ayaklar\335 s\237r\237yerek y\237r\237me ve parmaklar\335n para)Tj
0 -1.30001 TD
-0.015 Tc
0.054 Tw
[(s)-15(ayma hareketleri gibi semptomlar Fahr sendromlu hasta-)]TJ
0 -1.3 TD
0.037 Tw
(larda g\232r\237lebilir. Di\333er semptomlar distoni, istemsiz, h\335zl\335)Tj
T*
0.095 Tw
(ve ani hareketler ve n\232betleri i\215erir. Hastal\335k \215ocuklu\333un)Tj
T*
0.036 Tw
(erken d\232neminden ba\337layarak ya\337am\335n herhangi bir d\232ne-)Tj
T*
0.014 Tw
(minde ortaya \215\335kabilir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 399.5884 456.2517 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
0 Tw
((1))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 408.5526 453.6117 Tm
0 Tr
0 0 0 1 k
-0.0151 Tc
(.)Tj
0.4842 0 Td
-0.015 Tc
0.014 Tw
(Hastal\335\333\335n ba\337)Tj
5.4972 0 TD
0 Tc
(-)Tj
0.31776 0 TD
-0.015 Tc
(l\335ca nedeni birin-)Tj
-15.97332 -1.30001 TD
-0.012 Tc
0 Tw
(cil)Tj
1.32482 0 TD
0.122 Tw
(ya da postoperatif disparatiroidizmdir. Paratiroid dis)Tj
20.91953 0 TD
0 Tc
(-)Tj
-22.24435 -1.3 TD
-0.015 Tc
0 Tw
(fonksiyonu d\335\337\335ndaki nedenler nadirdir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 463.6907 430.2517 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
0 Tw
((2))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 472.655 427.6118 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
-16.0844 -2.6 TD
0.022 Tc
0.088 Tw
[(Hastal\335\333a tan\335 koymak)-360(i\215in s\335kl\335kla BT)-360(yeterlidir )]TJ
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 525.2341 404.2517 Tm
0 Tr
0 0 0 1 k
0.022 Tc
0 Tw
((2))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 535.0825 401.6118 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
-22.32715 -1.3 TD
-0.012 Tc
0.122 Tw
(Prognozu iyi de\333ildir. Kalsiyum ve fosfor metabolizma)Tj
22.24453 0 TD
0 Tc
(-)Tj
-22.24453 -1.3 TD
-0.001 Tc
0.111 Tw
(s\335n\335 d\237zeltmekle iyi sonu\215lar al\335nabilir. Progresif n\232ro-)Tj
T*
-0.015 Tc
0 Tw
(lojik bozulma genellikle sakatl\335k ve \232l\237mle sonu\215lan\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 523.222 365.2517 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
0 Tw
((1))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 532.1862 362.6118 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
ET
Q
q
BT
/F1 1 Tf
10 0 0 10 311.811 336.6117 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(OLGU)Tj
ET
Q
q
BT
/F3 1 Tf
9 0 0 9 311.811 313.6117 Tm
0 Tr
0 0 0 1 k
0.022 Tc
0.103 Tw
(13 ya\337\335nda erkek hasta el, ayak, y\237z, ve g\232z kapaklar\335nda)Tj
0 -1.11111 TD
0.003 Tc
0.122 Tw
(istemsiz hareketleri olmas\335 nedeniyle ba\337vurdu. Yakla\337\335k bir)Tj
T*
0.047 Tc
0.078 Tw
(ayd\335r \337ikayetlerinin oldu\333u ve giderek artt\335\333\335 \232\333renildi.)Tj
T*
0.005 Tc
0.12 Tw
(Ba\337vurdu\333u \232zel bir sa\333l\335k kurulu\337u taraf\335ndan antiepileptik)Tj
T*
0.007 Tc
0.117 Tw
(bir ila\215 ba\337lanan hastan\335n \337ikayetlerinin gerilememesi nede-)Tj
T*
0.011 Tc
0.114 Tw
[(niyle \215ekilen beyin tomografisinde (BT),)-375(yayg\335n kalsifikas-)]TJ
T*
0.005 Tc
0.12 Tw
(yonlar saptanmas\335 \237zerine taraf\335m\335za sevk edilmi\337. Hastan\335n)Tj
T*
0 Tc
0.057 Tw
(\232z ge\215mi\337inde 7 ya\337\335ndayken ge\215irilen pn\232moni d\335\337\335nda \232zel-)Tj
0 -1.11111 TD
0.003 Tc
0.122 Tw
(lik yoktu. Soyge\215mi\337inde baban\335n 37 ya\337\335ndayken miyokard)Tj
0 -1.11111 TD
0.007 Tc
0.118 Tw
(infarkt\237s\237 ge\215irdi\333i ve eksitus oldu\333u, k\237\215\237k karde\337inin ise)Tj
T*
(iki kez febril konv\237lziyon ge\215irdi\333i \232\333renildi. Fizik muaye)Tj
24.75319 0.00001 TD
0 Tc
(-)Tj
-24.75319 -1.11112 TD
0.066 Tw
(nesinde; \337uur a\215\335k, aktif, boy 140 cm \(3-10 p\), tart\335 32 kg \(3-)Tj
0 -1.11111 TD
0.034 Tw
(10 p\) idi. Hastan\335n koreoatetoik hareketleri g\232zlendi. Bilateral)Tj
T*
0.016 Tw
[(di\337li \215ark bulgusu vard\335 ve Babinski bulgusu negatif)-267(idi. Di\333er)]TJ
T*
0.025 Tw
(sistem muayenelerinde \232zellik yoktu. TA 110/70 mmHg, ate\337i)Tj
T*
0.044 Tw
(yoktu. G\232zdibi muayenesi normal olarak de\333erlendirildi. Tam)Tj
T*
0.07 Tw
(kan say\335m\335nda Hb 13.9 g/dl, Ht % 39.9, BK 11.000/mm)Tj
ET
Q
q
BT
/F3 1 Tf
7 0 0 7 518.9497 155.9217 Tm
0 Tr
0 0 0 1 k
0 Tc
(3)Tj
ET
Q
q
BT
/F3 1 Tf
9 0 0 9 522.4497 153.6117 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(,)Tj
0.56966 0 Td
0 Tc
0 Tw
(Plt)Tj
ET
0 0 0 0 k
56.693 627.796 481.89 100.708 re
f
Q
q
BT
/F1 1 Tf
20 0 0 20 57.6929 712.5873 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Fahr hastal\335\333\335)Tj
ET
Q
q
BT
/F1 1 Tf
10 0 0 10 57.6929 647.5873 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(Teoman AK\202AY (**), Meliha ARSLAN (*), Elif TOROS (*), Hasan \205NAL (**), Sevil SARIKAYA (**), )Tj
0 -1.3 TD
(Alper G\206ZELTA\336 (**), Erdal ADAL (***))Tj
ET
0 J 0 j 10 M []0 d 1 w
0 0 0 1 K
56.693 611.618 m
538.583 611.618 l
S
0 0 0 0 k
56.693 119.055 481.89 19.843 re
f
Q
q
BT
/F3 1 Tf
8 0 0 8 57.6929 131.6344 Tm
0 Tr
0 0 0 1 k
0 Tc
0.125 Tw
(SSK Bak\335rk\232y Do\333umevi Kad\335n ve \202ocuk Hastal\335klar\335 E\333itim Hastanesi, \202ocuk Sa\333l\335\333\335 ve Hastal\335klar\335, Asist. Dr.*; Uz. Dr.**; Klinik \336efi, Uz.)Tj
0 -1.125 TD
0 Tw
(Dr.*** )Tj
ET
0 J 0 j 10 M []0 d 1 w
0 0 0 1 K
56.693 143.89 m
538.583 143.89 l
S
57.78 755.355 m
539.669 755.355 l
S
0 0 0 0 k
56.693 752.851 481.89 13 re
f
Q
q
BT
/F1 1 Tf
10 0 0 10 57.6929 757.021 Tm
0 Tr
0 0 0 1 k
0.1 Tc
0 Tw
(OLGU SUNUMU)Tj
ET
Q
q
BT
/F3 1 Tf
10 0 2.12557 10 493.1929 757.021 Tm
0 Tr
0 0 0 1 k
0.1 Tc
0 Tw
(Pediatri)Tj
ET
0 J 0 j 10 M []0 d 1 w
0 0 0 1 K
56.693 748.351 m
538.583 748.351 l
S
56.693 771.024 m
538.583 771.024 l
S
56.693 270.04 m
283.465 270.04 l
S
0 0 0 0 k
56.693 789.197 127.626 10.173 re
f
Q
q
BT
/F2 1 Tf
8 0 0 8 57.6929 792.4114 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(G\232ztepe T\335p Dergisi 20(1):61-63, 2006)Tj
ET
0 0 0 0 k
526.249 92.168 12.334 12.714 re
f
Q
q
BT
/F1 1 Tf
10 0 0 10 527.2488 96.4236 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(61)Tj
ET
0 0 0 0 k
470.551 788.1971 68.027 11.1729 re
f
Q
q
BT
/F1 1 Tf
9 0 0 9 471.551 791.6577 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(ISSN 1300-526X)Tj
ET
Q
endstream
endobj
4 0 obj
<<
/Length 13439
>>
stream
/GS0 gs
q
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W n
1 g
0 841.89 0 0 re
f
Q
/GS1 gs
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0 0 0 0 k
56.693 119.055 481.89 637.796 re
f
Q
q
BT
/F3 1 Tf
9 0 0 9 57.6929 748.0599 Tm
0 Tr
0 0 0 1 k
0.01 Tc
0.115 Tw
(282.000/ mm)Tj
ET
Q
q
BT
/F3 1 Tf
7 0 0 7 107.7073 750.3699 Tm
0 Tr
0 0 0 1 k
0 Tc
(3)Tj
ET
Q
q
BT
/F3 1 Tf
9 0 0 9 111.2763 748.0599 Tm
0 Tr
0 0 0 1 k
0.0098 Tc
(,)Tj
0.6348 0 Td
0.01 Tc
0.115 Tw
(MCV 85 \265m)Tj
ET
Q
q
BT
/F3 1 Tf
7 0 0 7 165.3627 750.3699 Tm
0 Tr
0 0 0 1 k
0 Tc
(3)Tj
ET
Q
q
BT
/F3 1 Tf
9 0 0 9 168.9317 748.0599 Tm
0 Tr
0 0 0 1 k
0.0098 Tc
(,)Tj
0.63477 0 Td
0.01 Tc
0.115 Tw
(RDW % 12.6, periferik yay-)Tj
-12.99464 -1.11111 TD
0 Tc
0.093 Tw
(mas\335 ve l\232kosit form\237l\237 normaldi. ESR 15 mm/saat, CRP (-))Tj
T*
0.012 Tc
0.113 Tw
[(idi. Biyokimyasal tetkiklerinde;)-375(\237re 43 mg/dl, kreatinin 0.9)]TJ
-0.0001 Tc
(m)'
0.77793 0.00001 TD
0 Tc
0.012 Tw
[(g/dl, Na 135 mEq/l, K)-262(4.2 mEq/l, Ca)-262(7.0 mg/dl, P)-262(5.4 mg/dl,)]TJ
-0.77793 -1.11112 TD
-0.0002 Tc
(A)Tj
0.72183 0.00001 TD
0 Tc
0.086 Tw
[(LP)-336(550 U/L, ALT)-337(24 U/L, AST)-336(9 U/L, T.)-336(protein)-336(7.2 g/dl,)]TJ
-0.72183 -1.11111 TD
-0.0001 Tc
(a)Tj
0.44389 0.00001 TD
0 Tc
0.015 Tw
[(lbumin)-265(4.2 g/dl, GGT)-264(19 U/L, LDH)-265(405 U/L olarak bulundu.)]TJ
-0.44389 -1.11112 TD
0.013 Tc
0.112 Tw
[(T)1(e)1(k)1(r)1(a)1(r)1( )1<8D>1(a)1(l)1
111(l)1(a)1(n)1( )1(C)1(a)-374(7.2 mg/dl, P)-375(6.8 mg/dl olarak bulundu.)]TJ
0 -1.11111 TD
0.027 Tc
0.098 Tw
(Serum parathormon d\237zeyi 381 pg/ml olarak bulundu. 24)Tj
T*
0.015 Tc
0.11 Tw
(saatlik idrarda kalsiyum at\335l\335m\335 normal s\335n\335rlardayd\335. Seru-)Tj
T*
0.003 Tc
0.122 Tw
(loplazmin d\237zeyi 38.3 mg/dl (22-61mg/dl) idi. Amonyak 90)Tj
T*
0.02 Tc
0.105 Tw
(mg/dl, laktat 1.4 mg/dl (0.5-2.0) olarak bulundu. Hastan\335n)Tj
T*
0.024 Tc
0.101 Tw
(bat\335n US normal olarak de\333erlendirildi. \202ekilen MRG\325de;)Tj
0 Tc
'
0.44549 0.00001 TD
0.002 Tc
0.123 Tw
(her iki dentat nucleusta, her iki putamen ve caudat nucleus)Tj
-0.44549 -1.11112 TD
0.0023 Tc
(b)Tj
0.50231 0.00001 TD
0.002 Tc
(a\337\335nda T1 hiperintensitesi ile birlikte T2 a\333\335rl\335kl\335 kesitlerde)Tj
-0.50231 -1.11111 TD
0.0108 Tc
<9A>Tj
0.51084 0.00001 TD
0.011 Tc
0.114 Tw
(zellikle bazal gangliyonda simetrik sinyal art\335\337\335 ilk planda)Tj
-0.51083 -1.11112 TD
0 Tc
0.045 Tw
(toksik ve metabolik bozukluklara ba\333l\335 olabilir. Ay\335r\335c\335 tan\335da)Tj
0 -1.11111 TD
0.02 Tc
0.105 Tw
(hipoparatiroidi, hiperparatiroidi, mitokondrial bozukluklar,)Tj
T*
0.027 Tc
0.098 Tw
(hepatolenktik\237ler dejenerasyon d\237\337\237n\237lmelidir. Ek olarak)Tj
T*
0 Tc
0.099 Tw
(kalvaryal diploik mesafe ekspansiyonunun kronik anemik bir)Tj
T*
0.001 Tc
0.124 Tw
(pro\215ese sekonder geli\337mi\337 olabilece\333i d\237\337\237n\237ld\237\323 \337eklindey-)Tj
T*
0 Tc
0.112 Tw
(di. Hastan\335n kalsiyum de\333erinin d\237\337\237k, fosfat de\333erinin y\237k-)Tj
0 -1.11112 TD
0.081 Tw
(sek ve parathormon d\237zeyinin de y\237ksek olmas\335 \237zerine ps\232-)Tj
0 -1.11111 TD
0.076 Tw
(dohipoparatiroidi olabilece\333i d\237\337\237n\237ld\237. Tip tayini i\215in idrar-)Tj
T*
0.034 Tw
(da cAMP tetkik klini\333imiz \337artlar\335nda bak\335lamad\335\333\335ndan yap\335-)Tj
T*
0.009 Tw
(lamad\335. Hastaya kalsitriol ve kalsiyum laktat tedavisi ba\337land\335,)Tj
0 -1.11112 TD
0.033 Tc
0.092 Tw
(\337ikayetlerinde azalma g\232zlendi. Endokrinoloji ve geli\337im)Tj
0 -1.11111 TD
0 Tc
0 Tw
(n\232rolojisinden takip edilmek \237zere taburcu edildi. )Tj
ET
Q
q
BT
/F1 1 Tf
10 0 0 10 57.6929 462.0599 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(TARTI\336MA)Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 57.6929 436.0599 Tm
0 Tr
0 0 0 1 k
0.015 Tc
0.11 Tw
(\334ntrakraniyal multipl simetrik kalsifikasyonlar parati-)Tj
0 -1.3 TD
0 Tc
0.078 Tw
(roid disfonksiyonlar\335, sistemik hastal\335klar (SLE), intok-)Tj
T*
0.055 Tc
0.07 Tw
(sikasyonlar (karbonmonoksit), radrasyon, anoksi,)Tj
T*
0.003 Tc
0.122 Tw
(Cockayne\325s sendromu, ensefalit, Kearnes- Seayre sen-)Tj
T*
0 Tc
0.003 Tw
(dromu ve Fahr sendromunda ortaya \215\335kar )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 225.5858 386.6999 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((3,4))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 240.91 384.0599 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(.)Tj
0.50298 0 Td
0 Tc
0.003 Tw
(Beyin t\237-)Tj
-18.82469 -1.3 TD
0.001 Tc
0.124 Tw
(m\232rleri, gran\237lomat\232z hastal\335klar, )Tj
14.2666 0 TD
0 Tc
(i)Tj
0.27897 0 TD
0.001 Tc
(nfeksiyonlar, intok)Tj
7.69893 0 TD
0 Tc
(-)Tj
-22.2445 -1.30001 TD
0.012 Tc
0.113 Tw
(sikasyonlar gibi bilinen nedenlere ba\333l\335 olarak ortaya)Tj
0 -1.3 TD
0 Tc
0.022 Tw
(\215\335kan kalsifikasyonlar bilateral striopallidodentate kalsi-)Tj
T*
-0.012 Tc
0.122 Tw
(fikasyonlardan (BSPDC) ayr\335 olarak de\333erlendirilmekte)Tj
22.24443 0.00001 TD
0 Tc
(-)Tj
-22.24443 -1.3 TD
-0.004 Tc
0 Tw
(dir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 72.2773 321.6999 Tm
0 Tr
0 0 0 1 k
-0.004 Tc
0 Tw
((4,5))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 87.4395 319.06 Tm
0 Tr
0 0 0 1 k
-0.0041 Tc
(.)Tj
0.60576 0 Td
-0.004 Tc
0.114 Tw
(BSPDC ayr\335 literat\237rde hen\237z bir g\232r\237\337 birli\333i)Tj
-3.58042 -1.3 TD
-0.008 Tc
0.118 Tw
(olu\337mam\335\337t\335r. Histolojik bulgular\335yla ilk kez Bamberger)Tj
T*
0.012 Tc
0.098 Tw
(taraf\335ndan 1855\325te tan\335mlanan bilateral simetrik bazal)Tj
T*
0.025 Tc
0.084 Tw
(gangliyon ve serebellar n\237kleuslar\335n kalsifikas)Tj
20.14221 0.00001 TD
0 Tc
(-)Tj
0.35831 0.00001 TD
0.026 Tc
0 Tw
(yonu)Tj
-20.50052 -1.30001 TD
-0.015 Tc
0.047 Tw
(Fahr\325\335n 1930\325da yapt\335\333\335 bildirimden sonra Fahr sendromu)Tj
0 -1.3 TD
0.039 Tc
0.071 Tw
(olarak an\335lmaya ba\337lanm\335\337t\335r. Sonralar\335 sendromun)Tj
T*
-0.001 Tc
0.111 Tw
(BSPDC, hipoparatiroidi ve n\232ropsikiyatrik bulgulardan)Tj
T*
-0.015 Tc
0.098 Tw
(olu\337an bir triad\335 oldu\333u belirlenmi\337tir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 209.0373 230.6999 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
0 Tw
((6,7))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 223.7615 228.06 Tm
0 Tr
0 0 0 1 k
-0.0151 Tc
(.)Tj
0.5675 0 Td
-0.015 Tc
0.098 Tw
(Lowenthal ve)Tj
-17.17436 -1.3 TD
0.001 Tc
0.109 Tw
[(Bruyn,)-360(1968\325de )-1(ailesel)-360(serebral kalsifikasyonu 4 gruba)]TJ
T*
0.013 Tc
0 Tw
(ay\335rm\335\337lard\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 114.7 204.6999 Tm
0 Tr
0 0 0 1 k
0.013 Tc
0 Tw
((8))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 124.3503 202.06 Tm
0 Tr
0 0 0 1 k
0.013 Tc
0.097 Tw
[(:)-360-1(d)-1(i)-1(y)-1(o)-1(p)-1(a)-1(t)-1(i)-1(k)-1( ailesel)-361(hipoparatiroidizm,)]TJ
-6.66574 -1.3 TD
-0.015 Tc
0.092 Tw
(ps\232dohipoparatiroidizm ve ps\232dops\232dohipoparatiroidizm,)Tj
T*
-0.006 Tc
0.116 Tw
[(infantil ailesel)-360(olgular ve idiyopatik ailesel)-360(striopallido-)]TJ
T*
0.003 Tc
0.107 Tw
(dentate kalsifikasyon. Daha sonraki yay\335nlarda infantil)Tj
T*
-0.015 Tc
0.045 Tw
[(ailesel)-280(olgular\335n hemen \215o\333unun Cockayne\325s sendromuna)]TJ
T*
-0.002 Tc
0.111 Tw
(uydu\333u g\232r\237lm\237\337 ve bu adla an\335lmaya ba\337lanm\335\337t\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 271.6762 139.6999 Tm
0 Tr
0 0 0 1 k
-0.002 Tc
0 Tw
((9))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 280.9656 137.0599 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
-22.32727 -1.3 TD
-0.004 Tc
0 Tw
(Yine)Tj
1.92752 0.00001 TD
0 Tc
(,)Tj
0.60598 0.00001 TD
-0.004 Tc
0.114 Tw
(Fahr sendromu )Tj
6.44763 0.00001 TD
0 Tw
(ad\335n\335n)Tj
2.83539 0.00001 TD
0.114 Tw
(kullan\335lmamas\335 gerekti\333ini)Tj
13.59529 62.28869 TD
-0.015 Tc
0 Tw
(s\232yleyenler de vard\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 395.4106 749.587 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
0 Tw
((5))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 404.3748 746.9471 Tm
0 Tr
0 0 0 1 k
-0.015 Tc
(.)Tj
-9.25638 -2.6 TD
0.031 Tc
0.093 Tw
[(Geni\337 serili postmortem bir incelemede,)-376(birincil)-375(si-)]TJ
0 -1.3 TD
0.004 Tc
0.121 Tw
(metrik bazal gangliyon kalsifikasyonlar\335n\335n s\335kl\335\333\335 on-)Tj
T*
0 Tc
0.124 Tw
(binde 2.7 olarak bildirilmi\337tir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 437.2224 697.587 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((10))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 450.5652 694.947 Tm
0 Tr
0 0 0 1 k
0.0005 Tc
(.)Tj
0.62542 0 Td
0 Tc
0.124 Tw
(BT ile yap\335lan yine)Tj
-14.50084 -1.3 TD
0.052 Tw
[(geni\337 serili iki \215al\335\337mada ise,)-302(bazal ganglionlar\335n simet-)]TJ
T*
0.011 Tw
(rik kalsifikasyonlar\335n\335n s\335ras\335yla % 0.2 ve % 1.02 olarak)Tj
T*
0.007 Tw
(saptand\335\333\335, ancak s\335ras\335yla % 0.1 ve % 0.2\325sinde n\232rolo-)Tj
-0.0001 Tc
(j)'
0.2779 0.00001 TD
0 Tc
0.069 Tw
(ik klinik bulgular\335n tabloya e\337lik etti\333i bildirilmektedir)Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 311.811 632.587 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((11,12))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 335.1352 629.9471 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(.)Tj
0.54626 0 Td
0 Tc
0.046 Tw
(Bunlar\335n i\215inde Fahr sendromuna uyan olgular\335n)Tj
-2.87868 -1.30001 TD
0.011 Tw
(s\335kl\335\333\335 konusunda bir bilgi yoktur. Bu klinik, radyolojik,)Tj
0 -1.3 TD
0.027 Tc
0.098 Tw
(biyokimyasal ve patolojik sonu\215lara dayanarak, idi-)Tj
T*
0.007 Tc
0.117 Tw
(yopatik, \215o\333unlukla ailesel, ekstrapiramidal semptom-)Tj
T*
0 Tc
0.056 Tw
(lara giden, hipoparatiroidizm olsun ya da olmas\335n, bila-)Tj
T*
0.091 Tw
(teral yayg\335n striatopallidodentate kalsifikasyonlar \(Fahr)Tj
T*
0.004 Tc
0.121 Tw
(sendromu\) ayr\335 bir antite olarak de\333erlendirilmekte ve)Tj
0 -1.30001 TD
0 Tc
0 Tw
(nadir g\232r\237lmektedir.)Tj
0 -2.6 TD
0.006 Tc
0.119 Tw
(Paratiroid disfonksiyonlar\335nda intrakraniyal kalsifikas-)Tj
0 -1.30001 TD
0.002 Tc
0.123 Tw
(yon olmadan da parkinsonizm tablosu g\232r\237lebilmekte-)Tj
0 -1.3 TD
0 Tc
0.125 Tw
(dir. Bunun)Tj
4.7802 0 TD
(da temelinde n\232rotransmisyon bozulmas\335na)Tj
-4.7802 -1.3 TD
0.007 Tc
0 Tw
(yol)Tj
1.67286 0 TD
0.118 Tw
(a\215an G protein defekti gibi ba\337ka patolojilerin ol)Tj
20.57148 0 TD
0 Tc
(-)Tj
-22.24434 -1.30001 TD
0 Tw
(du\333u san\335lmaktad\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 391.2348 463.587 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((13))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 404.5591 460.947 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
-9.27481 -2.6 TD
0.117 Tw
(Sendromda kalsifikasyonun arteriyol, ven\237l ve kapiller)Tj
0 -1.3 TD
0.001 Tc
0.124 Tw
[(perivask\237ler mesafede ba\337lad\335\333\335 ve kalsiyumun)-375(yan\335s\335-)]TJ
T*
0 Tc
0.036 Tw
(ra, demir, bak\335r, \215inko, fosfor, klor\237r, alim\237nyum, mag-)Tj
T*
0.02 Tw
(nezyum, potasyum, silikon, mukopolisakkarit, glikopro)Tj
22.2444 0 TD
(-)Tj
-22.2444 -1.3 TD
0.097 Tw
(tein ve nadir bir\215ok maddenin birikti\333i bildirilmektedir)Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 311.811 372.587 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((5,14,15))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 341.1352 369.947 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(.)Tj
0.58512 0 Td
0 Tc
0.085 Tw
(BT ile basal gangliyonlarda kalsifikasyon g\232s-)Tj
-3.51754 -1.3 TD
0.069 Tw
(terilen bir \215al\335\337mada, hastalara \215ekilen d\237z X-ray grafi)Tj
22.24439 0 TD
(-)Tj
-22.24439 -1.3 TD
0.076 Tw
(de ancak % 4 hastada kalsifikasyon g\232sterilebilmi\337. Bu)Tj
T*
0.009 Tc
0.116 Tw
(da BT\325den \232nceki devirlerde paratiroid disfonksiyonu)Tj
T*
(ve kalsifikasyon aras\335ndaki ili\337kinin oldu\333undan daha)Tj
T*
0 Tc
0.088 Tw
[(az olarak anla\337\335lmas\335na neden olmu\337tur. Ayr\335ca,)-338(bu \215a-)]TJ
T*
0.01 Tc
0.115 Tw
(l\335\337mada BT\325deki kalsifikasyonlar\335n derecesi ile klinik)Tj
T*
0 Tc
0.056 Tw
(ve laboratuvar bulgular\335 korele olarak bulunmu\337tur )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 521.7585 281.587 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((12))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 535.0827 278.9471 Tm
0 Tr
0 0 0 1 k
0 Tc
(.)Tj
-22.32717 -1.3 TD
0.006 Tc
0.119 Tw
(MRG ve serebellar dentate n\237kleuslarda farkl\335 oldu\333u)Tj
T*
0 Tc
0 Tw
(g\232sterilmi\337tir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 367.6371 255.5871 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((14))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 380.9613 252.9471 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(.)Tj
0.50038 0 Td
0 Tc
0.001 Tw
(Hastal\335\333\335n et)Tj
5.08233 0.00001 TD
(i)Tj
0.27783 0.00001 TD
(yopatogenezinde serbest)Tj
-12.77557 -1.30002 TD
0.011 Tc
0.113 Tw
(radikaller ve sitoplazmik organellerde \(mitokondri ve)Tj
0 -1.3 TD
0.023 Tc
0.102 Tw
(endoplazmik retikulum\) bozukluklar \237zerinde durul-)Tj
T*
0.031 Tc
0 Tw
(maktad\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 353.6244 216.5871 Tm
0 Tr
0 0 0 1 k
0.031 Tc
0 Tw
((5,16))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 374.4629 213.9471 Tm
0 Tr
0 0 0 1 k
0.0315 Tc
(.)Tj
0.65639 0 Td
0.031 Tc
0.093 Tw
(MRG\325de d\237\337\237k sinyal veren alanlar)Tj
-6.92157 -1.3 TD
0.017 Tc
0.108 Tw
(muhtemelen kalsiyum depolanmas\335n\335n erken evresini)Tj
T*
0.025 Tc
0.1 Tw
[(g\232sterir. Di\333er yandan,)-375(y\237ksek sinyal alanlar\335 endo-)]TJ
T*
0 Tc
0.024 Tw
(telyal membran yetersizli\333ine )Tj
12.20472 0 TD
0 Tw
(ikincil)Tj
2.8289 0.00001 TD
0.024 Tw
(olarak geli\337en pro)Tj
7.21078 0.00001 TD
(-)Tj
-22.2444 -1.30002 TD
0.002 Tc
0.123 Tw
(tein ve polisakkarit ya da s\335v\335 havuzlar\335yla olu\337ur. BT)Tj
0 -1.3 TD
0 Tc
0.091 Tw
[(semptomatik ya da asemptomatik, birincil)-342(ya da posto-)]TJ
T*
0.015 Tc
0.11 Tw
(peratif hipoparatiroidi hastalar\335nda bulunabilen kalsi)Tj
22.24448 0 TD
0 Tc
(-)Tj
-22.24448 -1.30001 TD
0.031 Tc
0.094 Tw
(fikasyonlar\335n b\237y\237kl\237\333\237n\237 ya da yerini g\232stermede)Tj
ET
0 0 0 0 k
410.956 789.197 127.627 10.173 re
f
Q
q
BT
/F2 1 Tf
8 0 0 8 411.9562 792.4114 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(G\232ztepe T\335p Dergisi 20(1):61-63, 2006)Tj
ET
0 0 0 0 k
56.693 92.168 12.334 12.714 re
f
Q
q
BT
/F1 1 Tf
10 0 0 10 57.6929 96.4236 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(62)Tj
ET
Q
endstream
endobj
5 0 obj
<<
/Length 9521
>>
stream
/GS0 gs
q
0 0.89 595 841 re
W n
1 g
0 841.89 0 0 re
f
Q
/GS1 gs
q
0 0 0 0 k
56.693 342.307 481.89 414.544 re
f
Q
q
BT
/F3 1 Tf
10 0 0 10 57.6929 748.021 Tm
0 Tr
0 0 0 1 k
-0.0001 Tc
(d)Tj
0.49992 0.00001 TD
0 Tc
0.122 Tw
[(aha iyidir. Di\333er yandan MRG)-372(de,)-371(T2 a\333\335rl\335kl\335 sinyal)]TJ
-0.49992 -1.30001 TD
0.037 Tw
(yo\333unlu\333unun artm\335\337 ya da azalm\335\337 oldu\333u durumlarda,)Tj
0 -1.3 TD
0.0331 Tc
(k)Tj
0.5331 0.00001 TD
0.033 Tc
0.092 Tw
(alsiyum birikiminin \215e\337itli evrelerini tan\335mlamada)Tj
-0.5331 -1.30001 TD
0 Tc
0 Tw
(daha muktedir g\232r\237lmektedir.)Tj
0 -2.6 TD
0.007 Tc
0.118 Tw
(Sendromun otozomal resesif, otomosal dominant, X\325e)Tj
0 -1.3 TD
0 Tc
0.019 Tw
[(ba\333l\335 ge\215i\337 g\232steren formlar\335n\335n)-269(yan\335s\335ra,)-269(sporadik olgu-)]TJ
T*
0.01 Tc
0.115 Tw
(lar da bildirilmektedir )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 153.886 659.6611 Tm
0 Tr
0 0 0 1 k
0.01 Tc
0 Tw
((9,17))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 173.7134 657.021 Tm
0 Tr
0 0 0 1 k
0.0104 Tc
(.)Tj
0.6354 0 Td
0.01 Tc
0.115 Tw
(Bozuk genin 14. kromo-)Tj
-12.23745 -1.3 TD
0.022 Tc
0.103 Tw
(zomun uzun kolunda oldu\333u \237zerinde durulmaktad\335r)Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 57.6929 633.6611 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
((18))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 71.0262 631.021 Tm
0 Tr
0 0 0 1 k
0.0002 Tc
(.)Tj
0.6251 0 Td
0 Tc
0.125 Tw
(\202ocukluk ve yeti\337kin \215a\333\335 formlar\335 kal\335t\335m, klinik)Tj
-1.95843 -1.3 TD
0.009 Tc
0.116 Tw
(g\232r\237n\237m\237n ve progresyon \232zellikleriyle farkl\335l\335k g\232s-)Tj
T*
0.019 Tc
0.106 Tw
(terir. Yeti\337kin formunda kalsifikasyonlar\335n olu\337maya)Tj
T*
(ba\337lamas\335ndan 15-20 sene sonra, 4.-5. dekatta klinik)Tj
T*
0.029 Tc
0.096 Tw
(semptomlar ortaya \215\335kmaktad\335r )Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 196.8303 581.6611 Tm
0 Tr
0 0 0 1 k
0.029 Tc
0 Tw
((9))Tj
ET
Q
q
BT
/F3 1 Tf
10 0 0 10 206.8603 579.0211 Tm
0 Tr
0 0 0 1 k
0.0293 Tc
(.)Tj
0.65422 0 Td
0.029 Tc
0.096 Tw
(Hastal\335k parkin-)Tj
-15.57096 -1.3 TD
0.026 Tc
0.099 Tw
(sonizm, serebellar sendrom, mental gerileme, psi\337ik)Tj
T*
0.016 Tc
0.109 Tw
(semptomlar, epileptik n\232betler ve ensefalopati semp-)Tj
T*
0 Tc
0 Tw
(tomlar\335na yol a\215abilir.)Tj
0 -2.6 TD
0.009 Tc
0.116 Tw
(Koreoatetoik hareketlerle ba\337vuran hastam\335z, kraniyal)Tj
0 -1.30001 TD
0.027 Tc
0.098 Tw
(g\232r\237nt\237lenmelerinin kalsifikasyonla uyumlu olmas\335,)Tj
0 -1.3 TD
0.012 Tc
0.112 Tw
[(laboratuvar tetkiklerinde ps\232)-1(dohipoparatiroidi saptan-)]TJ
T*
0.029 Tc
0.096 Tw
(mas\335 \237zerine Fahr sendromu (BSPDC) olarak kabul)Tj
T*
0.004 Tc
0.121 Tw
(edildi. Hastan\335n di\333er yak\335nlar\335n\335n \232zellikle BT ile ta-)Tj
T*
0 Tc
0.09 Tw
(ranmas\335n\335n yeni olgular\335 ortaya \215\335karabilece\333i d\237\337\237n\237l-)Tj
T*
0 Tw
(mektedir.)Tj
ET
Q
q
BT
/F1 1 Tf
10 0 0 10 57.6929 410.021 Tm
0 Tr
0 0 0 1 k
0 Tc
0 Tw
(KAYNAKLAR)Tj
ET
Q
q
BT
/F1 1 Tf
8 0 0 8 57.6929 387.0211 Tm
0 Tr
0 0 0 1 k
0.009 Tc
0 Tw
(1.)Tj
ET
Q
q
BT
/F3 1 Tf
8 0 0 8 66.8309 387.0211 Tm
0 Tr
0 0 0 1 k
0.009 Tc
0.116 Tw
(National Institutes of Neurological disorders of Stroke, National)Tj
-1.14225 -1.25 TD
0 Tc
0 Tw
(Institutes of Health, 17.03.1999)Tj
ET
Q
q
BT
/F1 1 Tf
8 0 0 8 57.6929 367.021 Tm
0 Tr
0 0 0 1 k
0.024 Tc
0.101 Tw
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ET
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q
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21.31965 50.32076 TD
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ET
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(disorders of movement. In Joynt R.J. editor. Clinical neurology.)Tj
T*
0 Tc
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(Revised ed. Philadelphia JB Lippincott Company. 1992: Chapter 38)Tj
ET
Q
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ET
Q
q
BT
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0 Tr
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0.003 Tc
0.122 Tw
(temic metabolism of iron porphyrin and calcium in Fahr syndrome.)Tj
T*
0 Tc
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ET
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ET
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0.028 Tc
0.097 Tw
(Multidisciplinary diagnostoc approach to)Tj
-10.3563 -1.25 TD
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0.092 Tw
(Fahr\325s syndrome, a familial disease. Wien Klin Wochenschr 93:486-)Tj
T*
0 Tw
(489, 1981.)Tj
ET
Q
q
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ET
Q
q
BT
/F3 1 Tf
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0 Tr
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0.006 Tc
0.119 Tw
(Roentgen diagnostic of Fahr\325s disease.)Tj
-12.06933 -1.25 TD
0 Tc
0 Tw
(Rontgenblatter 36:194-196, 1983.)Tj
ET
Q
q
BT
/F1 1 Tf
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(8. Lowenthal A, Bruyn GW:)Tj
ET
Q
q
BT
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0 Tr
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0 Tc
0.008 Tw
(Calcification of striopallidodentate sys-)Tj
-12.39882 -1.25 TD
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(tem. In: Winken PJ, Bruyn GW,edittors. Handbook of clinical neurol-)Tj
T*
0 Tw
(ogy. New York:Elsevier Science, 1968, 703-729.)Tj
ET
Q
q
BT
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0 Tr
0 0 0 1 k
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ET
Q
q
BT
/F3 1 Tf
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0 Tr
0 0 0 1 k
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0.025 Tw
(Adult onset idiopathic famil-)Tj
-16.5649 -1.25 TD
0 Tw
(ial brain calcification. Arch Intern Med 2425-2427, 1984.)Tj
ET
Q
q
BT
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ET
Q
q
BT
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0.124 Tw
(Intracerebral non-arteriosclerotic vascular)Tj
-11.16925 -1.25 TD
0 Tc
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ET
Q
q
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(11. Goldscheider HG, Licshewski R, Claus D, Steribl W,)Tj
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ET
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q
BT
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T*
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ET
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ET
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0 Tc
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ET
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ET
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T*
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ET
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T*
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(mal recessive inheritance. Report of three siblings. Eur Neurol)Tj
T*
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(22(1):58-64, 1983.)Tj
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