. 1999; 5(2): 132-133 | |||
PEUTZ JEGHERS SYNDROMEAhmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi KliniğiPeutz - Jeghers Syndrome is a rare, inherited autozomal dominant disease characterized by gastrointestinal hamartomatous polyps and mucocutaneous pigmentation. In this paper we report two cases of Peutz -Jeghers syndrome who were admitted and operated with intussusception. Screening their family members revealed intestinal and extraintestinal manifestations of the disease and no malignancy was detected. Keywords: PEUTZ-JEGHERS SYNDROME, INTUSSUSCEPTIONPEUTZ JEGHERS SENDROMUAhmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi KliniğiAhmet Yılmaz, Kadri Güler, Hakan Bozkurtoğlu, Faik Çelik. PEUTZ JEGHERS SYNDROME. . 1999; 5(2): 132-133 |
|