. 2021; 51(2): 127-130 | |||
ANCA-Negative Churg-Strauss Syndrome Presenting as bilateral Central retinal artery occlusion: A Case ReportMalihe Nikandish1, Zeinab Saremi21Ophthalmology Department, Valiasr Hospital, Birjand University of Medical sciences, Birjand, Iran2Assistant Professor of Rheumatology, Internal Medicine Department, Valiasr Hospital, Birjand University of Medical sciences, Birjand, Iran. A 42-year-old man with an un-diagnosed CSS developed bilateral CRAO yet, was considered as the case in this paper. His medical history included only bronchial asthma and irregular prednisolone consumption, and no atherosclerotic risk factors. At presentation, visual acuity was Hand Motion (HM) in the right eye and Counting Fingers (CF) in left eye. Funduscopy represented retinal whitening and a cherry red spot in the right eye and also normal fundus in the left eye. After eyeball massage and systemic intra-ocular pressure lowering agents, Visual Acuity (VA) improved. On the 5th day of administration, he started suffering from right limb weakness and skin lesion as purpura on his right foot, which revealed mononeuritis multiple in electromyography. He had 52 percent eosinophilia shown in lab data. Based on hyper eosinophilia, bronchial asthma, mononeuritis multiplex vasculitis purpura, and sinusitis that had occurred in the process of the disease work up fulfilled the classification criteria by American College of Rheumatology for diagnosis of Churg–Strauss syndrome (CSS). Intravenous methylprednisolone was administrated 1g/day for 3 consecutive days and also 1g cyclophosphamide was started and continued monthly for 6 months. Foot drop and vasculitic purpura improved 7 days later; however, there was still no further improvement in visual acuity. In conclusion, In the presence of bilateral CRAO and lack of atherosclerotic risk factors, CCS should be considered as a predisposing factor, on which an appropriate investigation should be addressed. Keywords: Central Retinal Artery Occlusion, Anti Neutrophil Cytoplasmic Antibodies, Churg-Strauss SyndromeBilateral Santral retinal arter tıkanıklığı olarak ortaya çıkan ANCA-Negatif Churg-Strauss Sendromu: Bir Olgu SunumuMalihe Nikandish1, Zeinab Saremi21Oftalmoloji departmanı, Valiasr Hastanesi, Birjand Tıp Bilimleri Üniversitesi, Birjand, İran2Romatoloji Yardımcı Doçenti, İç Hastalıkları Bölümü, Valiasr Hastanesi, Birjand Tıp Bilimleri Üniversitesi, Birjand, İran. Öz Malihe Nikandish, Zeinab Saremi. ANCA-Negative Churg-Strauss Syndrome Presenting as bilateral Central retinal artery occlusion: A Case Report. . 2021; 51(2): 127-130 Corresponding Author: Zeinab Saremi, Iran |
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